HAILEY-HAILEY DISEASE – A CASE REPORT

ANJALY P NAIR; SIBY JOSEPH; LAKSHMI R; SUNU KURIAN

doi:10.22159/ajpcr.2020.v13i9.38690

Authors

ANJALY P NAIR Department of Pharmacy Practice, St. Joseph’s College of Pharmacy, Cherthala, Kerala, India.
SIBY JOSEPH Department of Pharmacy Practice, St. Joseph’s College of Pharmacy, Cherthala, Kerala, India.
LAKSHMI R Department of Pharmacy Practice, St. Joseph’s College of Pharmacy, Cherthala, Kerala, India.
SUNU KURIAN Department of General Medicine, Lourdes Hospital, Post Graduate Institute of Medical Science and Research, Ernakulam, Kochi, Kerala, India.

DOI:

https://doi.org/10.22159/ajpcr.2020.v13i9.38690

Keywords:

Familial pemphigus, Hailey-Hailey, ATP2C1 gene, Acantholysis, Dilapidated brick wall

Abstract

Hailey-Hailey disease (HHD) is a rare autosomal dominant skin condition discovered in 1939 by Hailey brothers. Prevalence is found to be around 1 in 50,000 and is relatively uncommon in India. First onset of disease occurs between 20 to 40 years of age, usually presented in the 3rd and 4th decades of life. Here, we report a case of a 50-year-old female who presented with clinical features of the HHD and showed greater response to the treatment.

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